J Korean Assoc Oral Maxillofac Surg 2018; 44(4): 198~203
Classical oral manifestations of Dyke-Davidoff-Masson syndrome: a case report with review of the literature
Ritesh Kalaskar1, Ashita Ritesh Kalaskar2
Departments of 1Pediatric & Preventive Dentistry and 2Oral Medicine & Radiology, Government Dental College & Hospital, Nagpur, India
Ritesh Kalaskar
Department of Pediatric & Preventive Dentistry, Government Dental College & Hospital, Medical College Premises, Medical Square, Nagpur 440003, India
TEL: +91-0712-2706899 E-mail: riteshpedo@gmail.com
ORCID: https://orcid.org/0000-0001-7403-3364
Received June 17, 2017; Accepted August 16, 2017.; Published online August 31, 2018.
© Korean Association of Oral and Maxillofacial Surgeons. All rights reserved.

This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/4.0/) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.
 Abstract
Dyke-Davidoff-Masson syndrome is a non-inherited rare condition that presents during childhood and is characterized by seizures, hemiplegia, mental retardation, cerebral hemiatrophy, calvarial thickening, and hyperpneumatization of the frontal sinuses. The present article highlights a case of a 12-year-old male child with additional clinical findings of café-au-late pigmentation and ocular lipodermoid. This is the first case report of Dyke-Davidoff-Masson syndrome to describe oral manifestations, such as unilateral delayed eruption of teeth, hypoplasia, and taurodontism, which could be unique and characteristic of this condition. Oral health care providers and physicians should be aware of these oral observations as dental referrals could warrant early dental prophylactic care and can be useful in diagnosing the possible time of injury and type of Dyke-Davidoff-Masson syndrome.
Keywords: Cerebral atrophy, Enamel hypoplasia, Open bite, Impacted deciduous tooth, Seizures


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31 August 2018
Vol. 44
No. 4 pp. 141~203

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